Spinal amyotrophia - group of the hereditary chronic diseases, described the progressing atrophic paresises caused by a lesion of forward horns of a spinal cord.

The children's spinal amyotrophia is shown on the first to year of a life. The first amaze muscles of a trunk and legs, later muscular groups are involved in process all. Fascicular twitchings are typical. Sensitivity and functions of a basin are not broken. In late stages of illness contractures and deformations of a skeleton develop. Effective treatment is not present; illness in some months or years leads to mors.

Good-quality spinal amyotrophia. Atrophic paresises appear at children's and youthful age more often. Mainly proximal departments of extremities are amazed. Gradually process weakens, but patients during many years can keep ability to independent movement. Paraclinic data tap changes, characteristic and for a neurogenic amyotrophia, and for a myodystrophy.